Familial Case of Darier Disease with Guttate Leukoderma: A Case Series from India
نویسندگان
چکیده
62 Indian Dermatology Online Journal | Volume 9 | Issue 1 | January‐February 2018 Sir, Darier disease [DD; Darier‐White disease or (dys) keratosis follicularis], is an autosomal dominant disorder of keratinization with characteristic dermatologic findings such as keratotic papules on the seborrheic regions, brittle nails and longitudinal erythronychia, and palmoplantar pitting. Hypopigmented macules (guttate leukoderma or predominantly “idiopathic guttate hypomelanosis”) is known to be a rare finding in certain disorders of keratinization, e.g., DD, Grover disease, and Cole disease (guttate hypopigmentation with palmoplantar hyperkeratosis).[1,2] Here, we report 2 new cases of this association.
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